• Congenital, nonhereditary condition
  • Characterized by multiple enchondromatosis and multiple soft tissue hemangiomas
  • Skeletal lesions have the same distribution as Ollier’s
  • Recognized radiographically by calcified phleboliths (within the hemangiomatous lesions)
  • High risk of developing chondrosarcoma (usually low-grade) and/or soft tissue malignancies